Diseases [C] » Neoplasms [C04] » Neoplasms by Histologic Type » Neoplasms, Nerve Tissue » Nerve Sheath Neoplasms » Neurofibroma » Neurofibroma, Plexiform
Diseases [C] » Nervous System Diseases [C10] » Nervous System Neoplasms » Peripheral Nervous System Neoplasms » Nerve Sheath Neoplasms » Neurofibroma » Neurofibroma, Plexiform
Diseases [C] » Nervous System Diseases [C10] » Neuromuscular Diseases » Peripheral Nervous System Diseases » Peripheral Nervous System Neoplasms » Nerve Sheath Neoplasms » Neurofibroma » Neurofibroma, Plexiform
Description
A type of neurofibroma manifesting as a diffuse overgrowth of subcutaneous tissue, usually involving the face, scalp, neck, and chest but occasionally occurring in the abdomen or pelvis. The tumors tend to progress, and may extend along nerve roots to eventually involve the spinal roots and spinal cord. This process is almost always a manifestation of NEUROFIBROMATOSIS 1. (From Adams et al., Principles of Neurology, 6th ed, p1016; J Pediatr 1997 Nov;131(5):678-82) MeSH
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Phase 1 Indicated Drugs (1)
Organization Involved with Phase 2 Indications (29)
Organization Involved with Phase 1 Indications (4)
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UMLS Data
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